Protein ADHFE1  
 
Modifications:
In compartment: mitochondrial matrix
- ADHFE1@mitochondrial matrix 
 
 
Participates in complexes:
Participates in reactions:
As Reactant or Product:
As Catalyser:- (S)-2-hydroxyglutaric acid@mitochondrial matrix 
  + succinic semialdehyde@mitochondrial matrix 
  → 
  2-oxoglutaric acid@mitochondrial matrix 
  + 4-hydroxybutyrate@mitochondrial matrix 
 
 - 2-oxoglutaric acid@mitochondrial matrix 
  + 4-hydroxybutyrate@mitochondrial matrix 
  → 
  (S)-2-hydroxyglutaric acid@mitochondrial matrix 
  + succinic semialdehyde@mitochondrial matrix