Protein ADHFE1
Modifications:
In compartment: mitochondrial matrix
- ADHFE1@mitochondrial matrix
Participates in complexes:
Participates in reactions:
As Reactant or Product:
As Catalyser:- (S)-2-hydroxyglutaric acid@mitochondrial matrix
+ succinic semialdehyde@mitochondrial matrix
→
2-oxoglutaric acid@mitochondrial matrix
+ 4-hydroxybutyrate@mitochondrial matrix
- 2-oxoglutaric acid@mitochondrial matrix
+ 4-hydroxybutyrate@mitochondrial matrix
→
(S)-2-hydroxyglutaric acid@mitochondrial matrix
+ succinic semialdehyde@mitochondrial matrix